Search on: MITOCHONDRIAL TRIFUNCTIONAL PROTEIN 
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Descriptor English:   Mitochondrial Trifunctional Protein 
Descriptor Spanish:   Proteína Trifuncional Mitocondrial 
Descriptor Portuguese:   Proteína Mitocondrial Trifuncional 
Tree Number:   D08.811.520.241.300.250.249
D08.811.641.765
D08.811.682.047.820.150.707.249
D08.811.913.050.080.249
D12.776.543.602
D12.776.575.765
Definition English:   A mitochondrial protein consisting of four alpha-subunits and four beta-subunits. It contains enoyl-CoA hydratase, long-chain-3-hydroxyacyl-CoA dehydrogenase, and acetyl-CoA C-acyltransferase activities and plays an important role in the metabolism of long chain FATTY ACIDS. 
History Note English:   2014 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   55285 
Unique Identifier:   D063991 

Occurrence in VHL:
 

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